TY - JOUR
T1 - Cystic fibrosis related diabetes
T2 - Nutrition and growth considerations
AU - Kaminski, Beth A.
AU - Goldsweig, Bracha K.
AU - Sidhaye, Aniket
AU - Blackman, Scott M.
AU - Schindler, Teresa
AU - Moran, Antoinette
N1 - Funding Information:
The authors would like to thank the Cystic Fibrosis Foundation and the faculty mentor members of the EnVision: Emerging Leaders in CF Endocrinology Program, for their ongoing support and mentorship of the program awardees.
Publisher Copyright:
© 2019 European Cystic Fibrosis Society
PY - 2019/10
Y1 - 2019/10
N2 - Nutritional considerations are crucial to the optimal management of cystic fibrosis related diabetes (CFRD). The development of abnormal glucose tolerance and CFRD can have negative effects on CF nutritional status. Treatment of CFRD with insulin replacement is essential; however, medical nutrition therapy is important to maintain nutritional status while normalizing blood glucose levels. CF Foundation Nutritional Guidelines are recommended for the nutritional management of CFRD; specifically, the diet should be high in calories, protein, fat, and salt. Carbohydrate intake is not limited, but carbohydrate counting can be used to guide insulin dosing and maintain consistent blood glucose levels. CFTR modulator therapy shows early promise for the improvement of growth and nutritional parameters in CF.
AB - Nutritional considerations are crucial to the optimal management of cystic fibrosis related diabetes (CFRD). The development of abnormal glucose tolerance and CFRD can have negative effects on CF nutritional status. Treatment of CFRD with insulin replacement is essential; however, medical nutrition therapy is important to maintain nutritional status while normalizing blood glucose levels. CF Foundation Nutritional Guidelines are recommended for the nutritional management of CFRD; specifically, the diet should be high in calories, protein, fat, and salt. Carbohydrate intake is not limited, but carbohydrate counting can be used to guide insulin dosing and maintain consistent blood glucose levels. CFTR modulator therapy shows early promise for the improvement of growth and nutritional parameters in CF.
KW - Cystic fibrosis
KW - Cystic fibrosis related diabetes
KW - Growth
KW - Nutrition
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U2 - 10.1016/j.jcf.2019.08.011
DO - 10.1016/j.jcf.2019.08.011
M3 - Article
C2 - 31679727
AN - SCOPUS:85073664926
SN - 1569-1993
VL - 18
SP - S32-S37
JO - Journal of Cystic Fibrosis
JF - Journal of Cystic Fibrosis
ER -