Dentatorubro‐pallidoluysian atrophy of the myoclonus epilepsy type with posterior column degeneration

Ronald F. Pfeiffer, Rodney D. McComb

Research output: Contribution to journalArticlepeer-review

20 Scopus citations


Dentatorubro‐pallidoluysian atrophy (DRPLA) has a variable clinical presentation but the pathology is routinely confined to cerebellifugal and pallidofugal systems. We present a case of DRPLA of the myoclonus epilepsy type in which prominent posterior column degeneration was added to the pathological picture. This case illustrates the concept that the neurodegenerative diseases can be a continuum of both clinical and pathological presentations.

Original languageEnglish (US)
Pages (from-to)134-138
Number of pages5
JournalMovement Disorders
Issue number2
StatePublished - 1990


  • Dentatorubro pallidoluysian atrophy
  • Neurodegenerative disease
  • Ramsay Hunt syndrome

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology


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