Hearing loss in children with primary ciliary dyskinesia

Kathryn L. Kreicher, Heather K. Schopper, Akash N. Naik, Jonathan L. Hatch, Ted A. Meyer

Research output: Contribution to journalArticle

5 Scopus citations

Abstract

Objectives To evaluate the type and severity of hearing impairment in pediatric patients with primary ciliary dyskinesia (PCD) and relate these measures to patient demographics, treatment options, and other otologic factors. Methods A retrospective analysis of children with a diagnosis of PCD, Kartagener's syndrome, or situs inversus in the AudGen Database was conducted. Audiograms were analyzed for type of hearing loss (HL), severity, laterality, and progression. Medical charts were reviewed to identify factors that influence severity and progression of hearing loss. Results 56 patients met inclusion criteria and 42 patients had HL. 66.6% had bilateral and 33.3% had unilateral loss (70 total ears with HL). Conductive hearing loss (CHL) was the most common type of HL, though 30% of children had some sensorineural component to their hearing loss. 92.9% of children with HL received at least one diagnosis of otitis media, but HL did not improve in the majority (77.8%) of ears in our study regardless of ear tube placement. Conclusions Slight to mild CHL and all types of otitis media are prevalent among patients with PCD, and some of these children have sensorineural hearing loss (SNHL). All patients diagnosed with situs inversus at birth should be evaluated by an otolaryngologist.

Original languageEnglish (US)
Pages (from-to)161-165
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume104
DOIs
StatePublished - Jan 2018

Keywords

  • Pediatric hearing loss
  • Primary ciliary dyskinesia

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Otorhinolaryngology

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