Abstract
Four inherited disorders known to effect major arteries will be discussed, including Marfan syndrome (MS), Ehlers-Danlos syndrome (EDS), bicuspid aortic valve (BAV) and nonsyndromic familial aortic dissection. Recent advances in understanding their pathophysiology are presented, and how this knowledge impacts on diagnosis, prevention and treatment is discussed.
Original language | English (US) |
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Pages (from-to) | 185-188 |
Number of pages | 4 |
Journal | Cardiovascular Pathology |
Volume | 14 |
Issue number | 4 |
DOIs | |
State | Published - Jul 2005 |
Keywords
- Aneurysm
- Aorta
- Bicuspid valve
- Dissection
- Ehlers-Danlos syndrome
- Marfan syndrome
- Nonsyndromic familial aortic dissection
ASJC Scopus subject areas
- Pathology and Forensic Medicine
- Cardiology and Cardiovascular Medicine