Mitral Annular Disjunction Associated With Fatal Ventricular Arrhythmia in an Adolescent With Marfan Syndrome

Karen Carr, Anji Yetman, Ruchira Garg

Research output: Contribution to journalArticlepeer-review

Abstract

We discuss an adolescent with Marfan syndrome and a previous aortic valve-sparing root replacement who was found to have mitral annular disjunction on surveillance cardiac imaging in the setting of recurrent palpitations. Ambulatory heart rate monitoring incidentally captured a fatal ventricular arrhythmia, a well-recognized but underappreciated cause of sudden cardiac death in patients with Marfan syndrome. (Level of Difficulty: Advanced.)

Original languageEnglish (US)
Pages (from-to)1551-1556
Number of pages6
JournalJACC: Case Reports
Volume3
Issue number13
DOIs
StatePublished - Oct 6 2021

Keywords

  • Marfan
  • arrhythmia
  • connective tissue disorder
  • mitral annular disjunction
  • sudden cardiac death

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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